Urolog. pro Praxi, 2008; 9(3): 128-132
Retroperitoneal fibrosis (RPF) is an uncommon autoimmune collagen vascular disease of unclear aetiology. It is characterised by a chronic non-specific inflammation of the retroperitoneum, which can entrap and obstruct retroperitoneal structures, notably the ureters with a high risk of chronic renal failure. This comprehensive review deals with the various aspects of RPF and tries to provide a framework for the diagnosis, treatment and follow-up of this intriguing condition. There is no consensus until now which modality of a treatment (surgical or conservative) should be the method of the first choice. Although early diagnosis and treatment provide excellent renal and patient outcome, long-term follow-up is mandatory in all cases.
Published: June 1, 2008 Show citation
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